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Atypical superior semicircular canal dehiscence case report

The Egyptian Journal of Otolaryngology volume 29, pages 209–215 (2013)Cite this article

Abstract

Superior canal dehiscence syndrome is a rare medical condition with many variants. In this case report, we present a 35-year-old patient who presented with atypical presentation of superior canal dehiscence syndrome. We discuss his audiological, vestibular, and radiological findings before and after surgery. We present a protocol to establish the diagnosis of a similar condition, especially those presenting atypically.

References

  1. Minor LB, Solomon D, Zinreich JS, Zee DS. Sound- and/or pressure-induced vertigo due to bone dehiscence of the superior semicircular canal. Arch Otolaryngol Head Neck Surg. 1998;124:249–258.

    Article  CAS  Google Scholar 

  2. Minor LB. Superior canal dehiscence syndrome. Am J Otol. 2000;21:9–19.

    Article  CAS  Google Scholar 

  3. Minor LB, Cremer PD, Carey JP, Della Santina CC, Streubel S-O, Noah WEG. Symptoms and signs in superior canal dehiscence syndrome. Ann N Y Acad Sci. 2001;942:259–273.

    Article  CAS  Google Scholar 

  4. Minor LB. Clinical manifestations of superior semicircular canal dehiscence. Laryngoscope. 2005;115 (10 I): 1717–1727.

    Article  Google Scholar 

  5. Murray M. Old bone collection reveals basis for some dizziness. The Hopkins Gazette 8 March 1999; Vol. 28: NO. 25.

  6. Duffy J. The clue in the old bones. Hopkins Medical News 1999. Available at: http://www.hopkinsmedicine.org/hmn/S99/mu_8.html.

  7. Albuquerque W, Bronstein AM. ‘Doctor, I can hear my eyes’: report of two cases with different mechanisms. J Neurol Neurosurg Psychiatry. 2004;75:1363–1364.

    Article  CAS  Google Scholar 

  8. Hopkins Medicine — symptoms & diagnosis of SCDS & ménière’s disease. Available at: http://www.hopkinsmedicine.org/Otolaryngology/vestibular/patients.html.

  9. Hirvonen TP, Carey JP, Liang CJ, Minor LB. Superior canal dehiscence: mechanisms of pressure sensitivity in a chinchilla model. Arch Otolaryngol Head Neck Surg. 2001;127:1331–1336.

    Article  CAS  Google Scholar 

  10. Carey JP, Hirvonen TP, Hullar TE, Minor LB. Acoustic responses of vestibular afferents in a model of superior canal dehiscence. Otol Neurotol. 2004;25:345–352.

    Article  Google Scholar 

  11. Brantberg K, Bergenius J, Mendel L, Witt H, Tribukait A, Ygge J. Symptoms, findings and treatment in patients with dehiscence of the superior semicircular canal. Acta Otolaryngol. 2001;121:68–75.

    Article  CAS  Google Scholar 

  12. Rhoton AL Jr., Pulec JL, Hall GM, Boyd AS Jr. Absence of bone over the geniculate ganglion. J Neurosurg. 1968;28:48–53.

    Article  Google Scholar 

  13. Minor LB, Carey JP, Cremer PD, Lustig LR, Streubel S-O, Ruckenstein MJ. Dehiscence of bone overlying the superior canal as a cause of apparent conductive hearing loss. Otol Neurotol. 2003;24:270–278.

    Article  Google Scholar 

  14. Mikulec AA, McKenna MJ, Ramsey MJ, Rosowski JJ, Herrmann BS, Rauch SD, et al.. Superior semicircular canal dehiscence presenting as conductive hearing loss without vertigo. Otol Neurotol. 2004;25:121–129.

    Article  Google Scholar 

  15. Halmagyi GM, McGarvie LA, Aw ST, Yavor RA, Todd MJ. The click-evoked vestibulo-ocular reflex in superior semicircular canal dehiscence. Neurology. 2003;60:1172–1175.

    Article  CAS  Google Scholar 

  16. Cremer PD, Minor LB, Carey JP, Della Santina CC. Eye movements in patients with superior canal dehiscence syndrome align with the abnormal canal. Neurology. 2000;55:1833–1841.

    Article  CAS  Google Scholar 

  17. Halmagyi GM, Curthoys IS, Cremer PD, Henderson CJ, Todd MJ, Staples MJ, D’Cruz DM. The human horizontal vestibulo-ocular reflex in response to high-acceleration stimulation before and after unilateral vestibular neurectomy. Exp Brain Res. 1990;81:479–490.

    Article  CAS  Google Scholar 

  18. Cremer PD, Halmagyi GM, Aw ST, Curthoys IS, McGarvie LA, Todd MJ, et al.. Semicircular canal plane head impulses detect absent function of individual semicircular canals. Brain. 1998;121:699–716.

    Article  Google Scholar 

  19. Watson SRD, Halmagyi GM, Colebatch JG. Vestibular hypersensitivity to sound (Tullio phenomenon): structural and functional assessment. Neurology. 2000;54:722–728.

    Article  CAS  Google Scholar 

  20. Streubel S-O, Cremer PD, Carey JP, Weg N, Minor LB. Vestibular-evoked myogenic potentials in the diagnosis of superior canal dehiscence syndrome. Acta Otolaryngol Suppl. 2001;545:41–49.

    Article  CAS  Google Scholar 

  21. Sheykholeslami K, Schmerber S, Kermany MH, Kaga K. Vestibular-evoked myogenic potentials in three patients with large vestibular aqueduct. Hear Res. 2004;190 (1–2): 161–168.

    Article  Google Scholar 

  22. Hillman TA, Kertesz TR, Hadley K, Shelton C. Reversible peripheral vestibulopathy: the treatment of superior canal dehiscence. Otolaryngol Head Neck Surg. 2006;134:431–436.

    Article  Google Scholar 

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Authors and Affiliations

  1. Department of Otorhinolaryngology, Faculty of Medicine, Audiology Unit, Alexandria University, 182 Omar Lofty Street Sporting Tram Station, Alexandria, 21111, Egypt

    Samir Asal MD

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  1. Samir Asal MD
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Correspondence to Samir Asal MD.

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Asal, S. Atypical superior semicircular canal dehiscence case report. Egypt J Otolaryngol 29, 209–215 (2013). https://doi.org/10.7123/01.EJO.0000432831.64017.8b

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  • DOI: https://doi.org/10.7123/01.EJO.0000432831.64017.8b

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