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A case of rhinolaryngoscleroma in a patient with neurofibromatosis type 1




Scleroma is a chronic-specific granuloma of the nose and it may involve other parts of the respiratory tract. The condition is endemic in Egypt. Neurofibromatosis type 1 (NF-1) is one of the most common genetic conditions of the nervous system. Before this report, no case had been published documenting scleroma in a patient with NF-1.


To describe a case of rhinolaryngoscleroma in a patient with NF-1.


Case report and literature review.


Presentation of clinical, imaging and pathological findings, as well as management considerations.


This is the first case to be reported in the literature documenting the coexistence of rhinolaryngoscleroma and NF-1. The biological events in the immune system await further studies.


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Correspondence to Kamal G. Effat.

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Effat, K.G. A case of rhinolaryngoscleroma in a patient with neurofibromatosis type 1. Egypt J Otolaryngol 29, 46–48 (2013).

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