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A case of rhinolaryngoscleroma in a patient with neurofibromatosis type 1

The Egyptian Journal of Otolaryngology volume 29, pages 46–48 (2013)Cite this article

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Abstract

Introduction

Scleroma is a chronic-specific granuloma of the nose and it may involve other parts of the respiratory tract. The condition is endemic in Egypt. Neurofibromatosis type 1 (NF-1) is one of the most common genetic conditions of the nervous system. Before this report, no case had been published documenting scleroma in a patient with NF-1.

Aim

To describe a case of rhinolaryngoscleroma in a patient with NF-1.

Methods

Case report and literature review.

Results

Presentation of clinical, imaging and pathological findings, as well as management considerations.

Conclusion

This is the first case to be reported in the literature documenting the coexistence of rhinolaryngoscleroma and NF-1. The biological events in the immune system await further studies.

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Authors and Affiliations

  1. Department of Otolaryngology, El-Sahel Teaching Hospital, Cairo, Egypt

    Kamal G. Effat

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  1. Kamal G. Effat
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Correspondence to Kamal G. Effat.

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Effat, K.G. A case of rhinolaryngoscleroma in a patient with neurofibromatosis type 1. Egypt J Otolaryngol 29, 46–48 (2013). https://doi.org/10.7123/01.EJO.0000423982.18447.fc

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  • DOI: https://doi.org/10.7123/01.EJO.0000423982.18447.fc

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