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Malignant peripheral nerve sheath tumour of the paranasal sinuses and the anterior skull base

Abstract

Malignant peripheral nerve sheath tumour represents 10% of all soft tissue sarcomas, only 10% of which occur in the head and neck, which makes it a rare entity.

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Hegab, A., Kenawy, M. & El-Amir, M. Malignant peripheral nerve sheath tumour of the paranasal sinuses and the anterior skull base. Egypt J Otolaryngol 28, 281–288 (2012). https://doi.org/10.7123/01.EJO.0000418459.98768.74

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  • DOI: https://doi.org/10.7123/01.EJO.0000418459.98768.74

Keywords

  • head and neck neoplasms
  • malignant peripheral nerve sheath tumours
  • neurofibromatosis type 1
  • paranasal sinus
  • skull base