Demographic data | No. (450) | (%) |
---|---|---|
Age (years) Mean ± SD (range) | 6.35 ± 2.00 (1–10) | |
Gender | ||
 Male | 205 | 45.6 |
 Female | 245 | 54.4 |
Family history of EVA | ||
 Yes | 80 | 17.8 |
 No | 370 | 82.2 |
History of hearing deterioration | ||
 Yes | 200 | 44.4 |
 No | 250 | 53.6 |
History of head trauma | ||
 Yes | 120 | 26.7 |
 No | 330 | 71.3 |
History of vestibular complaints | ||
 Yes | 100 | 22.3 |
 No | 350 | 77.7 |
Pattern of EVA | ||
 Isolated EVA | 346 | 76.9 |
 Part of Mondini anomalies | 104 | 23.1 |
Associated syndromes with EVA | 62 | 13.8 |
 Pendred’s syndrome (PS) | 35 | 7.8 |
 Branchiootorenal syndrome (BOR) | 12 | 2.7 |
 Distal renal tubular acidosis (RTA) | 5 | 1.1 |
 Waardenburg syndrome | 6 | 1.3 |
 CHARGE | 4 | 0.9 |